Enfermedad de Riga-Fede / Riga-Fede disease

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Management of prematurely erupted teeth in newborns.

The majority of natal and neonatal teeth are prematurely erupted primary teeth, whereas few are supernumerary in origin. They most commonly occur in mandibular central incisor region and often can lead to difficulty to the mother during breast feeding and tongue ulceration in newborn. Moreover, since majority of these have poorly developed roots and are mobile, there is always a fear of aspiration into respiratory passage. Extraction therefore is the most commonly rendered treatment for these teeth. This paper comprises cases of natal and neonatal teeth describing about their clinical characteristics and sequel. This paper has also highlighted the factor which needs to be considered during the management of natal/neonatal teeth and protocol followed at our centre.

Associação dos indicadores socioeconômicos, fatores pre e perinatais na ocorrência de defeitos de desenvolvimento de esmalte na dentição decídua: estudo de base populacional / Socioeconomic indicators, pre and perinatal factors associated with developmental defects of enamel in primary teeth: a population-based study

Os defeitos de desenvolvimento de esmalte (DDE) são alterações comuns na dentição decídua e podem estar associados a intercorrências nos períodos pré, peri e pós natais bem como a indicadores socioeconômicos. A literatura é escassa de evidências científicas de base populacional, sendo que a maioria das pesquisas é realizada principalmente com amostras específicas. O objetivo deste estudo foi estimar a prevalência de DDE em crianças de cinco anos de idade e verificar a associação com prematuridade, peso ao nascer, intercorrências na gravidez (síndrome hipertensivo, infeções urinarias e diabetes gestacional) e indicadores socioeconômicos (renda mensal per capita, escolaridade materna, tipo de escola frequentada pela criança). Realizou-se um estudo transversal representativo com uma amostra de 1350 crianças de cinco anos de idade em Belo Horizonte - MG. Brasil. Após o consentimento dos pais, as crianças foram examinadas para o diagnóstico do DDE utilizando os critérios do índice DDE modificado (FDI,1992), e, através de um questionário, as mães forneceram os dados socioeconômicos bem como peso ao nascer, tempo de gestação e às intercorrências durante a gravidez relacionadas a parto pre-termo e baixo peso. A análise dos dados foi realizada utilizando-se o programa SPSS para Windows versão 19.0 e incluiu a distribuição de frequência, qui-quadrado de Pearson e Teste Exato de Fisher e regressão de Poisson com variância robusta adotando um valor de p <0,05. A prevalência de DDE foi de 40,6%. A opacidade demarcada foi o tipo de defeito mais frequente (22,7%) Através da análise bivariada, verificou-se associação estatisticamente significativa entre o DDE e gênero, peso ao nascer, idade da mãe durante a gestação, escolaridade materna, intercorrência na gravidez (síndrome hipertensivo) e tipo de escola da criança. A partir do modelo de regressão de Poisson ajustado, observou-se maior prevalência de DDE entre as crianças do gênero masculino (RP: 1,177, 95% IC 1,033 ­ 1,342), com baixo peso ao nascer (RP: 1,387; 95% IC 1,161 ­ 1,656) e muito baixo peso ao nascer (RP: 1,667; 95% IC: 1,150 ­ 2,416). A partir destes resultados conclui-se que os defeitos de desenvolvimento de esmalte foram mais comuns entre as crianças do gênero masculino, com peso ao nascer baixo ou muito baixo

The developmental defects of enamel (DDE) are common changes in the primary dentition and may be associated with complications in the pre, peri and post-natal care as well as with socioeconomic indicators. Literature is scarce in scientific evidence in population base, once the majority of studies are mainly performed with specific samples. The aim of this cross-sectional study was to estimate the prevalence of DDE in five years old children and the association with premature, complications during pregnancy birth weight and socioeconomic indicators (family income, maternal education, type of preschool attended by children). A cross-sectional study was conducted with a representative sample of 1350 children of five years old of Belo Horizonte - MG. Brazil. After parental consent, children were examined for the diagnosis of DDE using DDE index modificated (FDI, 1992), and through a questionnaire mothers provided socioeconomic data, birth weight and premature and complications during pregnancy. Data analysis was performed using SPSS for Windows 19.0, and included frequency distribution, chi- square test and Fisher's exact test and Poisson regression with robust variance (p < 0.05). The prevalence of DDE was 40.6 %. The demarcated opacity was the most common type of defect (22.7%) by bi-variate analysis; there was also a statistically significant association between developmental defects of enamel and gender, weight birth, complications during pregnancy (Arterial hypertension), mother´s age in the pregnancy, maternal education, type of school of children. The Poisson regression model adjusted showed that there was a higher prevalence of enamel defects among male children (PR: 1.177, 95% CI 1.033 to 1.342), low weight (PR: 1.387, 95% CI 1.61 to 1.656) and very low (PR: 1.667, 95% CI: 1.150 to 2.416). Out of these results it is concluded that the development of enamel defects were more common among male children with low or very low birth weight

Diente natal / Natal teeth

INTRODUCCIÓN: se denominan dientes natales a aquellos dientes que se encuentran presentes en la cavidad bucal en el momento del nacimiento. Estos constituyen una alteración de erupción precoz y se presenta con más frecuencia en la región de los incisivos centrales inferiores. Dichos dientes pueden ocasionar trastornos en la alimentación, ulceraciones traumáticas sublinguales llamada entonces enfermedad de Riga-Fede y preocupaciones en cuanto a la posible aspiración de los mismos. OBJETIVO: describir las características de una niña con diente natal y los aspectos más relevantes del diagnóstico y tratamiento. PRESENTACIÓN DEL CASO: a la consulta de odontopediatría se presentó una madre con una niña de un mes de nacida, remitida del Servicio de Pediatría debido a la sospecha de presencia de un diente en el momento de su nacimiento. Dada la dificultad para la lactancia, la gran movilidad del diente y el alto riesgo de desprendimiento, el tratamiento aplicado fue la EXODONCIA. CONCLUSIONES: el caso presentó un diente natal pequeño y con ningún desarrollo radicular. El tratamiento aplicado fue exodoncia por el grado de movilidad del diente y forma cónica y puntiforme que tenía riesgo de desprendimiento. Por tener un mes de nacida no existía peligro de deficiencia de la coagulación resultante de la síntesis insuficiente de vitamina K que ocurre en los primeros días de vida. Aunque la presencia de diente natal es infrecuente es de gran importancia el conocimiento del diagnóstico y tratamiento del diente natal para el estomatólogo(AU)

INTRODUCTION: natal teeth are defined as those teeth that are present in the mouth at the time of birth. Natal teeth form an alteration of early eruption; generally the lower temporary central incisors are the most common tooth affected. These teeth are rare anomalies in newborns that can cause feed disturbances, tongue ulceration (Riga-Fede disease) and risk of aspiration of them. OBJECTIVE: the aim of this paper is to present a case report of a newborn girl with neonatal tooth and the most relevant aspects concerning the diagnosis and treatment. CLINIC CASE: a30 -day-old female baby was brought to our department, because she had one tooth at birth. Due to the great mobility it was decided to extract the mobile natal teeth. COMMENT: natal teeth, in most cases are small and with poor root development. The treatment of these teeth will depend on the degree of tooth mobility and presence of sharp incisal edge.The extraction must do after of the first weeks, because the vitamin K levels are low in the first days after birth and this is very important for the clot formation(AU)

Conservative management of Riga-Fede disease.

Riga-Fede disease presents in early infancy and is characterized by firm, verrucous plaques arising on the oral mucosal surfaces or tongue due to repetitive trauma. Treatment focuses on eliminating the source of trauma. The purpose of this report is to present a case involving preservation of the natal teeth using a protective mouthguard. At the follow-up, the ulcer had healed and the infant was feeding without difficulties.

Natal and neonatal teeth: a review of 23 cases.

Natal teeth erupt in utero, whereas neonatal teeth present during the first month of life. The lower central incisors are the most frequently affected teeth. The etiology is unknown, and the choice of treatment depends on several factors. The purpose of this paper is to review 23 cases of children with natal or neonatal teeth who attended a dental care program in a university maternal and infant oral health clinic. There was no gender predilection. Most were natal teeth (83 percent) and presented a mild degree of mobility (64 percent). Only two patients had breast-feeding difficulties (nine percent). Tooth maintenance was the most common treatment of choice (64 percent), and only two patients presented Riga-Fede disease (nine percent).

[Riga-Fede disease: traumatic ulceration of the tongue in an infant]. / Maladie de Riga-Fede: ulcération traumatique de la langue chez un nourrisson.

INTRODUCTION: Riga-Fede disease is rare. It is an oral mucosal ulceration due to repetitive dental trauma. We report the case of an infant for whom a quick diagnosis prevented many complications. OBSERVATION: A 45-day-old infant was brought to our consultation for pain during baby-bottle intake, preventing feeding. Oral examination revealed ulceration on the ventral surface of the tongue, associated next to a mandibular incisor present at birth. Pain stopped immediately after dental extraction of the supernumerary tooth. The infant could be fed again without any problem. The ulceration healed in less than three months. DISCUSSION: The diagnosis of Riga-Fede disease is strictly clinical. The early diagnosis in our case allowed for a quick management and normal feeding before there was any somatic consequence. Dental trauma is the most frequent cause of Riga-Fede disease. Treatment is conservative (polishing, resin) except in case of supernumerary teeth or excessive mobility. In these cases, extraction is indicated. The pathological diagnosis is required only when there is no healing after appropriate management fails, to look looking for another diagnosis.

Preauricular sinus, nephrolithiasis, infantine eczema and natal tooth: a new association.

Preauricular sinuses (ear pits) are common congenital abnormalities. The incidence of preauricular sinus is widely varied. Usually asymptomatic, they manifest as small hollows adjacent to the external ear near the anterior margin of the ascending limb of the helix, most frequently on the right side. Preauricular sinuses can be either inherited or sporadic. They may be bilateral, increasing the likelihood of being inherited, in 25-50% of cases. Preauricular sinuses are features of other conditions or syndromes in 3-10% of cases, primarily in association with deafness and branchio-oto-renal (BOR) syndrome. When other congenital anomalies coexist with these sinuses, auditory testing and renal ultrasound should be considered. A girl, who was three months and 20 days old, was presented because of the co-existence of a right infected preauricular sinus, nephrolithiasis, infantile eczema and a natal tooth.

Estenosis congénita del orificio piriforme y megaincisivo central único / Congenital nasal pyriform aperture stenosis and solitary maxillary central incisor: Case report

La estenosis congénita del orificio piriforme es una anomalía descrita recientemente en la literatura, provocada por un crecimiento excesivo de la apófisis ascendente del hueso maxilar, pudiendo ocasionar problemas respiratorios y alimenticios desde el periodo neonatal. Presentamos el caso de una recién nacida diagnosticada de esta patología asociada a un megaincisivo central único. La actitud elegida fue la observación, junto con la aplicación de medidas conservadoras. Un año después del diagnóstico, la paciente tiene un adecuado desarrollo ponderoestatural (AU)

Congenital nasal pyriform aperture stenosis has recently been described in the literature. It is caused by an upward overgrowth of the maxillary bone apophysis and may cause breathing and feeding problems from the neonatal period on. We present the case of a newborn girl diagnosed with this pathology associated with a solitary maxillary central incisor. Observation with conservative measures was the attitude chosen. One year after diagnosis the patient shows adequate height and weight development (AU)

Dente neonatal: relato de caso clínico / Neonatal tooth: case report

Este trabalho tem como objetivo apresentar um caso clínico de dente neonatal, em uma criança de um mês de idade, do sexo masculino, gemelar, atendida em um consultório particular. Apresenta também uma revisão de literatura sobre alguns aspectos mais importantes relacionados à etiologia dos dentes neonatais, prevalência e tratamento

Supernumerary tooth with associated dentigerous cyst in an infant. A case report and review of differential diagnosis.

This paper reviews the topic of dental structures present at birth or erupting prior to the deciduous incisor teeth. A literature review shows a prevalence of one in every 2000 live births. At this rate of occurrence it is likely that the general dental practitioner may be called upon to offer advice. This review is supported by the presentation of an unusual case of a supernumerary maxillary incisor tooth with the hallmarks of a neonatal tooth and the development of a soft tissue dentigerous cyst. The differential diagnosis of soft and hard tissue swellings in infants is also presented together with rare syndromal associations of natal and neonatal teeth.

Lesiones estomatológicas desde el nacimiento hasta los tres años / Oral lesions from birth to three years of age

Con el propósito de que el odontólogo que atiende niños pueda comprender y retener las distintas características de las lesiones, hemos dividido este trabajo en dos períodos distintos de su desarrollo físico. Todo lo expuesto aquí es un resumen de 30 años de trabajo junto a odontólogos y médicos que dirigen las distintas especialidades afines a la estomatología pediátrica. Este período lo hemos dividido en dos partes: Primera parte a) Lesiones que afectan al niño desde el nacimiento hasta los doce meses de vida. Quistes de Queratina (Nódulos de Bohn, Perlas de Epstein y quistes de la lámina dental). b) Lesiones névicas-angiomas y lesiones pigmentarias. Segunda parte: Nos hemos dedicado a las manifestaciones de las enfermedades producidas por virus, hongos y bacterias. Queremos alcarar que estas lesiones pueden aparecer en otra etapa de la vida del niño. Al final de la segunda parte mencionamos lesiones propias de los labios (queilitis) y de la lengua (glositis) (AU)

Congenital hydrocephalus associated with congenital glaucoma and natal teeth.

We report the first described association of natal teeth with congenital hydrocephalus and congenital glaucoma, anterior segment dysgenesis with non-attachment of the retina. The clinical findings support a diagnosis of Walker-Warburg syndrome. The forkhead 7 transcription factor gene is proposed as a candidate gene for this syndrome.

Primary congenital glaucoma and erupted teeth (natal teeth) in the newborn: a report of two cases.

Primary congenital glaucoma may be associated with several ocular, adnexal, and systemic abnormalities. Presented are two cases of primary congenital glaucoma that were associated with natal teeth; ie, the teeth were present in the oral cavity at the time of birth. To the knowledge of the author, this is the first report on the association of primary congenital glaucoma and natal teeth.

[Dentes natales]. / Dentes natales.

As an introduction, this article describes the circumstances under which dental anatomy was taught to first year students at Utrecht University on November 26, 1945, as this led to the observation of a dens natalis. Relevant literature is discussed concerning the significance of the dens natalis for the child's future and for the family. Investigations into the frequency of the phenomenon are mentioned. Variations of the phenomenon are discussed in two cases. An overview of feeding and eating difficulties and measures to be taken concludes the article.

Dentes natais: relato de três casos clínicos / Natal teeth: report of three clinical cases

Os autores apresentam três casos de dentes natais comprometendo os incisivos centrais inferiores em duas crianças do sexo masculino e em uma do sexo feminino. Nas do sexo masculino, ambos os dentes estavam envolvidos, sendo indicada a exodontia devido a mobilidade, complicaçöes periodontais e fenômeno doloroso quando da amamentaçäo, apesar de essas condiçöes variarem de expressäo entre os casos. No terceiro caso, representado pela criança do sexo feminino, o elemento dentário foi o 71, o qual apresentava-se com grande mobilidade e alteraçöes periodontais, somando-se a vigência da doença de Riga-Fede, motivos pelos quais também foi indicada a exodontia. A histologia dos dentes avulsionados revelou, como achado comum, pouco desenvolvimento radicular e malformaçäo dentinária

[(Neo)natal tooth inperspective. Literature review and report of two cases]. / De (neo)natale tand in perspectief. Literatuuroverzicht en twee casus.

The 'problem' of the (neo)natal tooth is discussed in conjunction with a report of two cases and a review of the literature. The estimated incidence is between 1:700 and 1:3500 births. Girls are more often affected than boys. It usually concerns the two lower central deciduous incisors. The cause is most likely to be a superficial position of the tooth-germ, in which a hereditary component is a positive factor. The tooth is often deficient and very mobile, which may require treatment. In these cases extraction is the best therapy, if necessary after administration of vitamin K.

Natal molars in Pfeiffer syndrome type 3: a case report.

The following report is the first documented case of natal teeth associated with a recently described new entity, Pfeiffer syndrome type 3. The clinical manifestations consistent with the spectrum of this rare disorder are described with an emphasis on the concomitant natal teeth. Pfeiffer syndrome type 3 is one of the craniosynostosis syndromes and has been described in only two patients to date. Both mandibular incisors and maxillary molar natal teeth were found. Natal teeth are teeth, which are present in the oral cavity at birth. They are often associated with developmental abnormalities and recognized syndromes. Their incidence ranges from 1 in 2,000 to 3,500 births. The natal teeth found in this infant included both the mandibular primary incisors and maxillary primary first molars bilaterally. The clinical and histological considerations of natal teeth and their management are discussed. The presence of multiple natal teeth is extremely rare.

[Anomalies of the oral cavity in Mexican neonates]. / Anomalías de la cavidad oral en neonatos mexicanos.

The results of 1,200 physical oral cavity examinations in neonates born at the National Institute of Perinatology (INPer) are reported here, finding the frequency of occurrence of inclusion cysts, natal and neonatal teeth. We found that 46% (551 neonates) of those examined had inclusion cysts, among which the Bohn nodules were the most frequent (36 cases); a case of natal teeth was found as well as 30 cases of neonatal teeth. We emphasize the importance of these findings to both the pediatrician and the dentist since they constitute a frequent motive for visits during the perinatal period.